Abstract
and importance: Infantile hemangioma, being a benign tumor of the blood vessel, is part of a triad composed of also thrombocytopenia and hypofibrinogenemia as part of Kasabach Merrit Syndrome.
We report the case of a 2 months old female Saudi infant referred due to respiratory distress, thrombocytopenia, and enlarging hemangioma on right upper chest, neck, and lower cheek. Diagnosis of kaposiform hemangioendothelioma complicated by Kasabach Merritt thrombocytopenia was done based on the clinical triad of thrombocytopenia, bleeding tendency, and the presence of a vascular tumor.
Vincristine and CTA embolization are lines of management that showed to be the most efficient in the improvement of the clinical picture of KMS in our patient.
•KMS is a rare syndrome and rapid diagnosis is essential for enhanced prognosis.•A wide range of life-threatening complications can occur rapidly.•Utilization of vincristine CTA embolization showed dramatic improvement in patient's symptoms.•KMS necessitates utilizattion of different treatment modalities and a multi-disciplinary team approach.