Abstract
Marfan syndrome is an autosomal dominant genetic disorder of connective tissue origin that can affect multiple organs. Various oral manifestations have been associated with this syndrome. Hypohyperdontia is a condition of mixed numeric variations that presents a combination of hypodontia with hyperdontia within a single human dentition. The purpose of this paper is to report a case of Marfan syndrome with a concomitant occurrence of hypohyperdontia. A narrative review was also included to describe the other syndromes that had been associated with concomitant hypohyperdontia.