Abstract
Thoracic ectopic kidney is the rarest type of ectopic kidney with a reported finding of one in every 15,000 autopsies. The diagnosis of this anomaly is often incidental. Children may be symptomatic with recurrent respiratory symptoms. We present a case of an infant with a thoracic ectopic kidney associated with a congenital diaphragmatic hernia that was initially misdiagnosed as unresolved pneumonia due to persistent well-demarcated opacity in the left lower lobe. Our aim is to increase awareness about this rare entity.