Abstract
Ectodermal dysplasia (ED) is a rare hereditary syndrome that is categorized by the nonstandard development of certain tissues and structures of ectodermal origin. This disorder is important to dentists because it affects teeth and results in hypodontia or anodontia. Young children who are affected by ED and anodontia face functional and aesthetic difficulties due to the deficiency of teeth. Restoring lost vertical dimension and teeth with a removable prosthesis improves speech, aesthetics, and appearance and thus boosts the patient's self-confidence. We report a case of hypohidrotic ED with an oligodontia (absence of all primary teeth except upper second primary molars) in a 5-year-old female patient who was successfully rehabilitated with conventional removable dentures in the maxillary and mandibular arches using multidisplinary approach. The goal of the treatments was to improve psychological development in addition to promoting aesthetics, speech, and eating effectiveness, as well as the overall improvement of the stomatognathic system. Previouslay, most of the ED cases were treated with removable prosthesis, either in form of partial pr complete removable prosthesis in both maxilaary as well as mandibular arches. These types of prosthesis were allowed for relaining and rebasing as most of the ED patients were receiving treatments during young ages. These days, with the improvements of dental materials and equipments, advance treatments with over denture implants have been introduced for replacement of missing teeth which are caused by ED The present case report along with an updated review discusses the successful dental management of the rare disorder.