Abstract
Introduction: Epidermolysis bullosa (EB) is a group of rare inherited disorders characterised by formation of blisters following minor trauma to the skin or mucosal surfaces. There are four major forms of EB-simple, junctional, dystrophic and Kindler syndrome. According to the form of EB, the oral and dental manifestations are varied in the frequency and severity. Case Report: A 6-years old girl with a dystrophic form of EB was attended in our dental care centre in 2018. On examination, the child had multiple blisters on her elbows, feet, knees. Clinical and radiographic examinations revealed multiple carious lesions affecting almost the present primary dentition, with moderate gingival inflammation. Treatment: The patient had oral hygiene and dietary instructions, restorative dental treatment, extraction of badly decayed teeth. The patient was routinely followed up every three months for up to 1 year. On the last recall visit, the patent presented with good oral health status.