Abstract
Dowling-Degos disease (DDD) is an uncommon autosomal dominant genodermatosis characterized by reticular hyperpigmentation in the intertriginous areas. Herein, we report a case of follicular DDD which is a very rare variant of DDD. A 45-year-old healthy male presented with 1-year-history of asymptomatic slowly progressive skin lesions in the axillae. Skin examination revealed multiple nonscaly pigmented follicular papules and macules in both axillae but more severe in the right side. No other skin lesions elsewhere in the body. Hair, nails, and mucus membrane were all normal. Skin biopsy showed follicular plugging with the presence of pigmented filiform rete ridges originating from the follicular epithelium. The patient was diagnosed as follicular DDD. The patient was reassured. Electrocautery treatment was used, which leads to a remarkable improvement of the lesions.