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Idiopathic nodular panniculitis in Niemann-Pick disease
Journal article   Peer reviewed

Idiopathic nodular panniculitis in Niemann-Pick disease

I Bukhari
Journal of the European Academy of Dermatology and Venereology, Vol.19(5), pp.600-602
09/2005
PMID: 16164717

Abstract

Betamethasone - therapeutic use Biopsy, Needle Drug Therapy, Combination Female Follow-Up Studies Fusidic Acid - therapeutic use Humans Immunohistochemistry Infant Niemann-Pick Diseases - complications Niemann-Pick Diseases - diagnosis Niemann-Pick Diseases - therapy Panniculitis, Nodular Nonsuppurative - complications Panniculitis, Nodular Nonsuppurative - diagnosis Panniculitis, Nodular Nonsuppurative - drug therapy Risk Assessment Severity of Illness Index Treatment Outcome
Idiopathic nodular panniculitis is a condition characterized by the recurrent appearance of inflammatory nodules in the subcutaneous fat. In this report, an infant affected with Niemann-Pick disease and recurrent lobular panniculitis is described and discussed.

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