Abstract
A large multicystic mass lesion is not a common presentation of pulmonary sequestration. This presentation may result in failure to identify the supplying systemic artery due to multiplicity of the large cysts and, therefore, a wrong diagnosis. We discuss a case of intralobar pulmonary sequestration presented similarly. Chest x-ray and CT appearance gave an initial impression of hydatid disease which is endemic in Saudi Arabia. Fortunately, the supplying systemic artery was identified in the final CT review before surgery. Preoperative correct diagnosis of pulmonary sequestration is important to plan the appropriate surgery and to prevent possible intractable intraoperative hemorrhage. Awareness of this uncommon presentation of pulmonary sequestration helps to prevent such a fatal complication.