Abstract
Neurenteric cysts are rare congenital intraspinal cysts of endodermal origin. Herewith reported is a case of a 17-year-old girl harbouring an isolated cervical (C1-C3) neurenteric cyst, with intradural extramedullary development and without mediastinal enterogenous cyst. Magnetic resonance imaging was diagnostic. Surgery by means of a cervical laminectomy resulted in total removal of the lesion compressing the spinal cord on its ventral aspect and in rapid relief of symptoms, that were cervicooccipital pain and lower limb weakness of 1-month duration.