Abstract
Kimura's disease is a rare condition and typically presents as
non-tender subcutaneous swellings in the head and neck region, usually
in the pre-auricular and submandibular areas. It is associated with
lymphadenopathy (both local and distal), marked peripheral
eosinophilia, and an elevated IgE level. It can easily be mistaken for
a malignant disorder. Fine needle aspiration can be misleading, and a
diagnosis is established only by histopathological examination. Renal
involvement, which may affect up to 60% of patients, is the only
systemic manifestation. We report a case of Kimura's disease in a
Malay patient who was associated with steroid-responsive nephrotic
syndrome.