Abstract
Klippel Trenaunay syndrome is a congenital syndrome characterized by varicosities presenting with skin pigmentations and limb hypertrophy. The incidence has been increasing in outpatient clinic. Although the management of Klippel Trenaunay syndrome is primarily nonoperative, the patients without any deep vein insufficiency can be operated. We believe that this disease group should be investigated further early detection, considering that the complications of the disease with increasing mortality including deep vein thrombosis and pulmonary embolism can be prevented.