Abstract
BACKGROUND: When treated in a dental chair, patients with deformities such as scoliosis often require special consideration. CASE REPORT: Here is a case of 9 years old Saudi child who was reported with dental prob-lems. The objective of this study is to provide a guideline for dental management of diastroph-ic dysplasia. CONCLUSIONS: Diastrophic dysplasia is a rare and nonlethal skeletal dysplasia, autoso-mal inheritance recessive, recognized by the in-fant's dysmorphic changes at birth. Diastroph-ic dysplasia is not a common hereditary disor-der, however, the characteristic of this condi-tion and guidelines for dental treatment should be known to a pediatric dentist, particularly at a major medical center.