Sign in
Back
The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia
Journal article   Open access

The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia

Raida Ben Salah, Mona Snoussi, Nour Louati, Chebbi Donia, Faten Frikha, Mnif Hela, Bahloul Zouhir and Mejdi Snoussi
Electronic journal of general medicine, Vol.15(5), p.em78
01/01/2018
DOI: https://doi.org/10.29333/ejgm/94112

Abstract

General & Internal Medicine Life Sciences & Biomedicine Medicine, General & Internal Science & Technology
Autoimmune Lymphoproliferative syndrome is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+CD4-CD8-) T cells (DNT) in the peripheral blood. Here we report the case of 19 years-old girl that was diagnosed as autoimmune Lymphoproliferative syndrome with a literature review.
url
https://doi.org/10.29333/ejgm/94112View
Published (Version of record) Open

Metrics

1 Record Views

Details