Abstract
Pachydermodactyly (PDD) is a rare, acquired idiopathic form of digital fibromatosis. PDD typically presents as asymptomatic swelling of the second to fourth proximal interphalangeal joints bilaterally in young males. Here, we present an acquired unilateral PDD in a Saudi boy with emphasis on the clinical, radiological, and histopathological features. In conclusion, PDD is a benign disease; a prompt recognition would prevent irrelevant workup and reassure patients.